It's 11 PM. Something feels off. You're not sure if it's serious. The doctor's office is closed. What do you do?

This decision tree helps you sort through that decision quickly. It's organized by symptom category and tells you whether to manage at home, call the nurse line, head to urgent care, or go to the ER.

Important caveat: When in doubt, call. This tree gives general guidance but doesn't replace clinical judgment. If something feels seriously wrong, get help.


The four levels of response

LEVEL 1 — HANDLE AT HOME
   Document, monitor, plan to discuss at next visit

LEVEL 2 — CALL THE NURSE LINE
   Within hours; get guidance on next step

LEVEL 3 — GO TO URGENT CARE / SAME-DAY VISIT
   Within hours; need evaluation today

LEVEL 4 — GO TO THE ER / CALL 911
   Now; potentially serious or life-threatening

Universal red flags — go to ER immediately

If ANY of these are present, skip the rest of this tree and go to the ER or call 911:

  • ☐ Difficulty breathing — significantly worse than baseline
  • ☐ Chest pain or pressure (in older children/adults)
  • ☐ Loss of consciousness or fainting
  • ☐ Severe dehydration / inability to keep fluids down
  • ☐ Severe bleeding that won't stop
  • ☐ Signs of stroke (facial droop, arm weakness, slurred speech)
  • ☐ Severe allergic reaction (swelling, difficulty breathing, hives spreading)
  • ☐ Suicidal thoughts with intent or plan
  • ☐ Severe abdominal pain
  • ☐ Pale or gray / blue color to lips, fingertips, face
  • ☐ Confusion or significant decrease in responsiveness
  • ☐ Seizure (first time, or different from usual pattern)

For these, going via 911 or by car (whichever is faster) is appropriate. Bring the ER Quick-Reference Card.


By symptom category

Cardiac symptoms

NEW SHORTNESS OF BREATH

☐ Severe / can't speak in full sentences
   → ER NOW

☐ Significant / new at rest or with usual activity
   → ER

☐ With swelling in legs, face, or abdomen
   → ER

☐ Lying flat is uncomfortable / need extra pillows
   → ER (may indicate heart failure decompensation)

☐ Mild and improves with rest
   → Call cardiology nurse line tomorrow morning

CHEST DISCOMFORT

☐ Crushing pressure radiating to arm/jaw
   → ER NOW (call 911)

☐ New, persistent (>20 minutes)
   → ER

☐ Brief, mild, with clear cause (cough, exertion)
   → Document; mention at next visit

PALPITATIONS

☐ With fainting, chest pain, severe shortness of breath
   → ER

☐ Persistent (>30 minutes) and new
   → ER or urgent care

☐ Brief, no other symptoms
   → Document; call cardiology if recurring

SUDDEN WEIGHT GAIN

☐ 3+ lb in 1-2 days
   → Call cardiology same day or next morning

☐ 5+ lb in a week
   → Call cardiology

Diabetes / metabolic symptoms

HYPOGLYCEMIA (LOW BLOOD SUGAR)

☐ Severe (<54 mg/dL or unconscious)
   → Glucagon if available; call 911 if not responsive
   → ER

☐ Moderate (55-69 mg/dL) with symptoms
   → Treat with fast carbs; recheck in 15 min
   → If recurring, call endocrinology

☐ Mild and resolved with treatment
   → Document; call endocrinology if pattern

HYPERGLYCEMIA (HIGH BLOOD SUGAR)

☐ With nausea/vomiting/abdominal pain (possible DKA)
   → ER

☐ Significantly high (>400 mg/dL) with no clear cause
   → Call endocrinology; possible ER

☐ Mildly elevated, expected (after meal, illness)
   → Document; manage per usual sick-day rules

KETONES POSITIVE

☐ Positive ketones with vomiting
   → ER (DKA risk)

☐ Positive ketones without vomiting
   → Call endocrinology

UNABLE TO KEEP DOWN INSULIN-DEPENDENT NUTRITION

☐ Vomiting >24 hours, can't keep liquids down
   → ER (dehydration risk, glucose management challenge)

Vision-related

SUDDEN VISION CHANGE

☐ Sudden complete loss of vision
   → ER (retinal detachment, stroke)

☐ Sudden new floaters with light flashes
   → Call ophthalmology same day; possible ER

☐ Sudden blurring or dimming
   → Urgent care or same-day ophthalmology

☐ Gradual change over weeks/months
   → Routine ophthalmology appointment

EYE PAIN / REDNESS

☐ Severe pain
   → ER or urgent care

☐ Trauma to the eye
   → ER

☐ Mild irritation
   → Document; monitor; call ophthalmology if persists

Respiratory symptoms

WORSENING ASTHMA / WHEEZING

☐ Severe — can't speak, blue lips, exhausted
   → ER (call 911)

☐ Moderate, not responding to inhaler
   → Urgent care or ER

☐ Mild, responsive to inhaler
   → Document; call pulmonology if pattern

PNEUMONIA-LIKE SYMPTOMS

☐ High fever + cough + difficulty breathing
   → ER or urgent care

☐ Cough + fever, can still breathe okay
   → Urgent care or call PCP same day

☐ Cough alone, no fever, no shortness of breath
   → Manage at home; call PCP if persists

CPAP NOT WORKING / BREATHING TROUBLE AT NIGHT

☐ Severe night-time breathing difficulty
   → ER

☐ CPAP malfunctioning, severe symptoms next day
   → Call sleep medicine same day

☐ CPAP malfunctioning, manageable
   → Document; troubleshoot per manual; call sleep medicine

Acute illness (fever, infection)

HIGH FEVER

☐ <3 months old with fever
   → ER

☐ Fever in patient with cardiac involvement, lethargy
   → Urgent care or call PCP same day

☐ Fever 102-104°F + significantly ill
   → Urgent care or call PCP

☐ Mild fever with normal energy
   → Manage at home; document

GASTRO ILLNESS (vomiting, diarrhea)

☐ With diabetic patient, can't keep down liquids
   → ER

☐ With cardiac patient, signs of dehydration
   → Urgent care

☐ Mild, drinking okay
   → Manage at home; sick-day rules for diabetes

URINARY TRACT INFECTION SYMPTOMS

☐ Fever + back pain (kidney involvement)
   → ER or urgent care

☐ Burning, frequency, no fever
   → Same-day urgent care or PCP

ABDOMINAL PAIN

☐ Severe, persistent, with vomiting
   → ER

☐ With high triglycerides history (pancreatitis risk)
   → ER

☐ Moderate, manageable
   → Call PCP same day or next

Mental health emergencies

SUICIDAL THOUGHTS WITH INTENT

→ Crisis line NOW
   • 988 (US — call or text)
   • Samaritans 116 123 (UK)
   • Crisis Text Line: text HOME to 741741
→ ER if person is unwilling/unable to call
→ Don't leave the person alone

PANIC ATTACK

☐ First-ever, severe, mimics cardiac symptoms
   → ER (rule out cardiac)

☐ Recurring, known pattern
   → Use coping plan; call therapist next day

DEPRESSIVE CRISIS / WITHDRAWAL

☐ Person not eating, not getting out of bed days
   → Call crisis line, mental health provider

☐ Severe distress without imminent risk
   → Call mental health provider next day

ANY UNUSUAL MENTAL STATE

☐ Confusion, hallucinations, severe agitation
   → ER (could be medical, psychiatric, or both)

Other situations

EQUIPMENT MALFUNCTION

CPAP / BiPAP not working
   → Document; call sleep medicine next business day
   → If breathing severely affected → urgent care

Hearing aid / cochlear implant not working
   → Document; troubleshoot; call audiology

Insulin pump malfunction
   → Switch to backup insulin (pen/syringe)
   → Call endocrinology

CGM not working
   → Switch to fingerstick glucose
   → Call endocrinology

MEDICATION ISSUES

Missed dose
   → Take when remembered if close to scheduled time
   → Skip if too close to next dose
   → Call pharmacy or PCP for guidance

Took double dose
   → Call poison control (1-800-222-1222 in US)
   → Or 111 (UK NHS)
   → Or pharmacist

Severe side effect
   → ER if respiratory, cardiac, neurological
   → Otherwise call PCP or pharmacy

NEW MEDICATION REACTION

Mild rash, no breathing issues
   → Stop the medication; call PCP/prescriber

Anaphylaxis (swelling, breathing trouble, hives)
   → Use EpiPen if available
   → Call 911

Decision tree, simplified version

For a quick sanity check:

    Is the person in immediate danger?
              │
        ┌─────┴─────┐
        ▼           ▼
       YES          NO
        │           │
     CALL 911       │
                    ▼
            Severe new symptom?
            (breathing, pain, mental status)
                    │
              ┌─────┴─────┐
              ▼           ▼
             YES          NO
              │           │
          GO TO ER       │
                         ▼
                Significantly worse than baseline?
                         │
                   ┌─────┴─────┐
                   ▼           ▼
                  YES          NO
                   │           │
              CALL NURSE       │
              LINE OR          ▼
              URGENT CARE  Manageable / known
                          pattern / mild?
                                │
                          ┌─────┴─────┐
                          ▼           ▼
                         YES          NO
                          │           │
                    HANDLE AT      Call PCP
                    HOME, monitor  next business
                                   day

Phone numbers to have ready

Pre-populate these and post on refrigerator, save in phone:

═══════════════════════════════════════════════════════════════
  KEY NUMBERS — POST WHERE FAMILY CAN FIND
═══════════════════════════════════════════════════════════════

  EMERGENCIES — 911 (US) / 999 (UK)

  CRISIS LINES:
  • 988 (US suicide & crisis lifeline)
  • Samaritans 116 123 (UK)
  • Text HOME to 741741 (US/UK/Canada Crisis Text Line)

  POISON CONTROL:
  • 1-800-222-1222 (US)
  • 111 (UK NHS)

  PRIMARY CARE / PEDIATRICIAN: ____________________________
  After-hours nurse line:      ____________________________

  CARDIOLOGY:                   ____________________________
  After-hours cardiology:       ____________________________

  ENDOCRINOLOGY:                ____________________________

  OPHTHALMOLOGY:                ____________________________

  AUDIOLOGY:                    ____________________________

  GENETICS:                     ____________________________

  CENTER OF EXCELLENCE:         ____________________________

  PHARMACY (24-hour):           ____________________________

  NEAREST CHILDREN'S ER:        ____________________________
  Address: ________________________________________________

  NEAREST ADULT ER:             ____________________________
  Address: ________________________________________________

  TRUSTED FAMILY/FRIEND HELP:   ____________________________
  ____________________________ ____________________________

═══════════════════════════════════════════════════════════════

What to bring when you go

If you're going to the ER or urgent care:

  • ☐ ER Quick-Reference Card filled in
  • ☐ Care binder
  • ☐ Current medication list
  • ☐ Insurance card
  • ☐ Phone charger
  • ☐ Snacks and water
  • ☐ Comfort item if it's a child

After the event

Whether you handled it at home, called the nurse, went to urgent care, or went to the ER:

Document

  • What happened
  • When
  • What you did
  • What the outcome was
  • What you'd do differently

Communicate

  • Update the primary care team if not already informed
  • Update the relevant specialist
  • Update the care binder

Reflect

  • Was the response appropriate?
  • Are there changes to home routines that would prevent recurrence?
  • Are there equipment, medications, or training that would help next time?

Plan

  • Bring up with the medical team at next visit
  • Update the after-hours plan based on what you learned
  • Address any underlying issue that contributed

When you're not sure

Default to calling. Most providers have a 24-hour nurse line or on-call physician for their patients. They'd rather hear from you than have you wait if something is serious.

Specifically when calling, share:

  • "This is the parent / patient with Alström Syndrome"
  • The specific symptom or concern
  • When it started
  • What you've already tried
  • What you're worried about
  • Your callback number

The nurse will help you triage to the right level of care.


Frequently Asked Questions

Should I call my specialist or go to ER first?

For severe symptoms, ER first; the ER can call the specialist. For moderate symptoms, calling the specialist's nurse line first lets them advise on whether ER is needed. For mild concerns, the nurse line is usually enough.

What if I'm overreacting?

Better to call and be told it can wait than not call and miss something. Medical teams expect to hear from families with rare conditions; they'd rather you check in.

What if it's the weekend?

Most major specialty offices have on-call coverage. Use the after-hours nurse line. For ER-level concerns, the ER works 24/7.

What about telehealth?

Some after-hours telehealth services exist (Teladoc, MDLIVE, hospital-affiliated services). They're useful for moderate concerns but can't replace ER for severe cases.

What if our specialists are far away?

Local urgent care or ER for acute issues; the local team can consult with your specialists. For non-acute matters, telehealth and phone consults work.


Related reading


This decision tree is for informational purposes only and is not a substitute for medical judgment. When in doubt, call the nurse line or go to the ER.